Erdheim-Chester disease of the central nervous system. Report of two cases. Review uri icon

Overview

abstract

  • The authors report two cases of Erdheim-Chester disease (ECD), an illness of unknown pathogenesis. Generally, this disease process involves the metaphyseal and diaphyseal portions of the long bones, the lungs, and the retroperitoneum; however, other tissues may be involved including the central nervous system (CNS). To date only two cases of CNS-related ECD have been reported. The present report adds to the literature by documenting two more recent cases of ECD involving the CNS. The clinical presentations of these cases, their radiological findings with special reference to magnetic resonance imaging, pathological determination, and clinical management are briefly reviewed.

publication date

  • May 1, 1997

Research

keywords

  • Central Nervous System Diseases
  • Granuloma
  • Histiocytosis

Identity

Scopus Document Identifier

  • 0031002236

Digital Object Identifier (DOI)

  • 10.3171/jns.1997.86.5.0888

PubMed ID

  • 9126908

Additional Document Info

volume

  • 86

issue

  • 5